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KMID : 1103920100160020176
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Korean Journal of Hepatology
2010 Volume.16 No. 2 p.176 ~ p.181
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Deficiencies in proteins C and S in a patient with idiopathic portal hypertension accompanied by portal vein thrombosis
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Hwang Se-Na
Kim Do-Young
Kim Min-Ju
Chon Young-Eun
Lee Hyun-Jung
Park Young-Nyun
Park Jun-Yong
Ahn Sang-Hoon
Han Kwang-Hyub
Chon Chae-Yoon
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Abstract
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Portal vein thrombosis (PVT) is an uncommon cause of presinusoidal portal hypertension. Among various hepatoportal disorders, noncirrhotic portal hypertension conditions such as idiopathic portal hypertension (IPH) are considered to have a close relation with PVT. PVT is known to have several predisposing conditions, including infection, malignancies, and coagulation disorders. There is growing interest and recognition that deficiencies in proteins C and S are associated with a hypercoagulable state. These deficiencies are regarded as key factors of systemic hypercoagulability and recurrent venous thromboembolism. We report the case of a 19-year-old male diagnosed as IPH with PVT and combined deficiencies in proteins C and S.
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KEYWORD
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Portal hypertension, Thrombosis, Protein C deficiency, Protein S deficiency
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